Familial 'benign' pemphigus? Erythroderma and fatal outcome

Autor: Tansini,Paula Baldissera, Boff,Ana Letícia, Weber,Magda Blessmann, Bonamigo,Renan Rangel
Jazyk: angličtina
Rok vydání: 2020
Předmět:
Zdroj: Anais Brasileiros de Dermatologia, Volume: 95, Issue: 1, Pages: 75-77, Published: 30 MAR 2020
Anais Brasileiros de Dermatologia v.95 n.1 2020
Anais brasileiros de dermatologia
Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
Popis: Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.
Databáze: OpenAIRE