Double outlet right ventricle {S,D,L} with subaortic ventricular septal defect and pulmonary stenosis

Autor: Van Praagh, Richard, Pérez-Trevino, Carlos, Reynolds, James L, Moes, C.A.F., Keith, John D., Roy, Douglas L., Belcourt, Christian, Weinberg, Paul M., Parisi, Lucy F.
Zdroj: The American Journal of Cardiology; January 1975, Vol. 35 Issue: 1 p42-53, 12p
Abstrakt: The clinical, hemodynamic, angiocardiographic and pathologic findings are presented in an infrequent but surgically correctable type of double outlet right ventricle. This study is based on six cases, one with autopsy confirmation. In all, the viscera and atria were in situs solitus (S). A ventricular d-loop was present (D). There was l-malposition of the great arteries, the aorta being to the left of, and anterior to, the pulmonary artery (L). Hence, this anomaly may conveniently be represented as double outlet right ventricle {S,D,L}. The ventricular septal defect was subaortic because the aorta was anterior and leftward, adjacent to the ventricular septum. A bilateral conus was present beneath both the aortic and pulmonary valves, preventing any semilunar-atrioventricular fibrous continuity. The subpulmonary conus was poorly expanded, resulting in pulmonary infundibular and valvular (annular) stenosis.
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