| Autor: |
POLSON, REX J., LIM, CHANG K., ROLLES, KEITH, CALNE, ROY Y., WILLIAMS, ROGER |
| Zdroj: |
Transplantation; September 1988, Vol. 46 Issue: 3 p386-388, 3p |
| Abstrakt: |
A 13-year-old boy who had had recurrent photosensitive skin reactions due to erythropoietic protoporphyria from 18 months of age, suddenly developed rapidly progressive hepatic failure with increasing cholestatic jaundice and variceal bleeding. Liver biopsy confirmed extensive protoporphyrin deposition with cirrhosis, and so orthotopic liver transplantation was performed. Postoperatively his skin rash settled within 72 hr, and in spite of subsequent exposure to the sun he has had no further skin reaction or blistering, although he does still have some itching. He made a good recovery and was able to return to school within six months of operation. |
| Databáze: |
Supplemental Index |
| Externí odkaz: |
|
