Heredopathia Atactica Polyneuritiformis (Refsum's disease) 1. Clinical features and dietary management

Autor: Masters-Thomas, Anne, Bailes, Janet, Billimoria, J. D., Clemens, M. E., Gibberd, F. B., Page, N. G. R.
Zdroj: International Journal of Food Sciences and Nutrition; August 1980, Vol. 34 Issue: 4 p245-250, 6p
Abstrakt: In a patient with Refsum's disease successful dietary control of the disease has been shown to depend on adequate energy and protein intake from phytanic acid-free sources and restriction of dietary phytanic acid to a maximum of 10 mg per day, with the provision of a generous amount of the essential fatty acid, linoleic acid. The present work gives data on the phytanic-acid content of various foodstuffs and suggests dietary manipulation of the patient.Although the role that chlorophyll-bound phytol plays in Refsum's disease is uncertain, it is advisable that this is eliminated until its role is more clearly identified.
Databáze: Supplemental Index