| Autor: |
de Terlizzi, Marino, Toma, Mario Grazia, Santostasi, Teresa, Colella, Roberto, Ceci, Adriana, De Benedicts, Giuseppe |
| Zdroj: |
Pediatric Hematology and Oncology; 1989, Vol. 6 Issue: 1 p37-44, 8p |
| Abstrakt: |
A case of angioimmunoblastic lymphadenopathy with dysproteinemia (AILD) in infancy is reported. The disease had a mild onset with generalized lymphadenopathy, hepatosplenomegaly, thrombocytopenia, polyclonal hypergammaglobulinemia, and T-cell deficiency. The AILD course lasted more than 100 months, alternating clinical remission to recurrent relapses. Hepatitis B viral infection suddenly evolving to hepatic failure was the cause of death. From a rapid survey of the present knowledge, the nosology, immunological features, and therapy of AILD are discussed and a possible presumptive pathogenetic pathway is proposed. |
| Databáze: |
Supplemental Index |
| Externí odkaz: |
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