The Placenta in Pseudoxanthoma Elasticum: Clinical, Structural and Immunochemical Study

Autor: Gheduzzi, D., Taparelli, F., Quaglino, D., Di Rico, C., Bercovitch, L., Terry, S., Singer, D.B., Pasquali-Ronchetti, I.
Zdroj: Placenta; July 2001, Vol. 22 Issue: 6 p580-590, 11p
Abstrakt: Pseudoxanthoma elasticum (PXE) is a rare genetic disorder clinically characterized by skin, cardiovascular and eye manifestations, mainly due to calcification and fragmentation of elastic fibres. Although infrequent, complications during pregnancy in women affected by PXE have been reported.
Databáze: Supplemental Index