| Autor: |
Washington, Ezella N., Placket, Timothy P., Gagliano Jr., Ronald A., Kavolius, Jeffery, Person, Donald A. |
| Předmět: |
|
| Zdroj: |
Hawaii Medical Journal; Aug2010, Vol. 69 Issue 8, p191-193, 3p |
| Abstrakt: |
Neurofibromatosis type 1 is an autosomal dominant disorder affecting the ras proto-oncogene. It is characterized by the overgrowth of nervous tissue and skin discoloration. While it is associated with a variety of phenotypic presentations, it is the plexiform variant that is particular concerning, as it can become extremely disfiguring and has a propensity for malignant degeneration. A case of a Pacific Islander with a large plexiform type 1 neurofibroma is presented. The patient was ultimately treated with surgical resection, negative pressure wound therapy, and split-thickness skin grafting with good results. A review of the literature concerning the diagnosis and treatment of neurofibromatosis is included. [ABSTRACT FROM AUTHOR] |
| Databáze: |
Supplemental Index |
| Externí odkaz: |
|
