| Abstrakt: |
Hereditary Hemorrhagic Telangiectasia (HHT), or Rendu-Osler-Weber syndrome, is a rare autosomal dominant disease characterized by mucosal, visceral, and dermal telangiectasias. This study details the case of a 68-year-old individual diagnosed with HHT since 2007. The patient has reported a progressive onset of telangiectasias on the face, oral mucosa, lips, palate, and tongue. In 2014 and 2018, the patient developed cerebral abscesses 15 days after dental manipulation for endodontic treatment. Additionally, episodes of epistaxis and gingival bleeding were noted, leading to sessions of vascular sclerotherapy on the oral mucosa under antibiotic prophylaxis. In 2022, the patient experienced hypovolemic shock necessitating volume resuscitation due to recurrent epistaxis and gingival bleeding. Following recovery, further sclerotherapy sessions were conducted. The patient is currently under follow-up, with plans for additional sclerotherapy sessions, and has not reported recent episodes of buccal bleeding. This case highlights the challenges and complications associated with HHT, emphasizing the importance of ongoing management and interventions to address the vascular manifestations of the syndrome. [ABSTRACT FROM AUTHOR] |
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