| Autor: |
Hyvönen, Hanna, Salminen, Päivi, Kallio, Milla, Lagus, Heli, Isoherranen, Kirsi |
| Předmět: |
|
| Zdroj: |
Journal of Wound Management; Nov2023, Vol. 24 Issue 3, p77-80, 4p |
| Abstrakt: |
Background Klippel-Trénaunay syndrome (KTS) is a rare congenital vascular malformation syndrome defined as capillary and venous malformations, and hypertrophy of the limb with or without lymphatic malformation. Currently there is no cure for KTS but the majority of patients are advised to wear compression garments on the affected limb to control swelling and discomfort. Aim To describe used compression therapy methods and their results in a paediatric patient with KTS. Methods The patient records were assessed for the used treatment methods for KTS. Our patient was treated with multimodal treatments to alleviate symptoms, and compression therapy was used specially to control lymphoedema and venous insufficiency. Results A 13-year-old boy with KTS had lymphoedema and venous insufficiency of the right lower extremity since birth. Compression therapy was started at the age of 2 months with a custom-made, single-leg compression pantyhose with gradual compression from distal to proximal regions. Furthermore, a manual lymphatic drainage and intermittent pneumatic compression were added on the regimen respectively. Other treatment methods included sclerotherapy, surgery and medication. None of treatment methods was sufficient alone to reduce limb oedema but the patient reported improved performance when using compression garments and a positive impact after enhanced compression therapy. Conclusion This report shows the importance of continuous and individualised compression therapy in the treatment of lymphoedema associated to KTS. [ABSTRACT FROM AUTHOR] |
| Databáze: |
Supplemental Index |
| Externí odkaz: |
|
