A lethal form of Gorham disease associated with extensive musculoskeletal pneumatosis: case report and review of the literature.

Autor: Omolola Atalabi, Steven Fishman, Harry Kozakewich, Ali Alsamarah, Ahmad Alomari
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Zdroj: Skeletal Radiology; Nov2008, Vol. 37 Issue 11, p1041-1046, 6p
Abstrakt: Abstract  We report here the imaging findings of a rare case of a lethal form of Gorham disease in a young female patient. Multimodality imaging findings over 13 year-follow-up demonstrated progressive wide spread skeletal and soft tissue abnormalities with permeative osteolysis, pathological fractures and severe skeletal deformities. Unusual extensive osseous and soft tissue pneumatosis was illustrated on cross-sectional studies. The progressive nature of this form of Gorham disease and the subsequent complications eventually culminated in patient’s death. [ABSTRACT FROM AUTHOR]
Databáze: Complementary Index