Niemann-Pick type III and Crohn's disease.

Autor: Joliffe, D. S., Sarkany, I.
Předmět:
Zdroj: Journal of the Royal Society of Medicine; Apr1983, Vol. 76 Issue 4, p307-308, 2p
Abstrakt: The article presents the case of a patient with Niemann-Pick disease who developed chronic perianal granulomata which is clinically and histologically characteristic of Crohn's disease. Niemann-Pick disease is a degenerative disorder associated with the accumulation of the lipid sphingomyelin in histiocytes, macrophages and reticulum cells within a wide range of tissues. There has been no previous recorded association between Niemann-Pick and Crohn's disease.
Databáze: Complementary Index