Clinical Characteristics of Children with Nasal BCOR-Rearranged Ewing-like Sarcoma: A Case Report and Literature Review.
| Autor: | Ji, Tingting, Li, Xiaodan, Li, Yanzhen, Zhang, Xuexi, Liu, Qiaoyin, Zhang, Jie, Sun, Nian, Liu, Zhiyong, Liu, Yuwei, Wang, Shengcai, Ni, Xin |
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| Předmět: |
NASAL surgery
NASAL cavity IMMUNOPHENOTYPING GENE rearrangement COMPUTED tomography SYMPTOMS NASAL tumors MAGNETIC resonance imaging ULTRASONIC imaging NOSE CANCER chemotherapy NEEDLE biopsy ONCOGENES EWING'S sarcoma SOFT tissue tumors CARTILAGE STAINS & staining (Microscopy) MOLECULAR pathology CHILDREN |
| Zdroj: | ENT: Ear, Nose & Throat Journal; Sep2024, Vol. 103 Issue 9, p548-553, 6p |
| Abstrakt: | Ewing-like sarcomas (ELS) are round cell mesenchymal neoplasms that are highly aggressive to bone and/or soft tissue. However, they rarely occur in the nose, with no reported such cases in the medical literature to date. Here, we reported the case of a two-year-old Chinese boy who presented with a mass in the left nasal cavity. Surprisingly, the final histopathological diagnosis of the nasal mass was determined to be a subtype of ELS, BCOR -rearranged sarcoma. Therefore, we retrospectively analyzed the clinical data of this case and reviewed the relevant literature on ELS and BCOR -rearranged sarcoma. The purpose of this article is to provide new insights into the clinical characteristics of children with BCOR -rearranged Ewing-like sarcoma and to improve the understanding of this disease. [ABSTRACT FROM AUTHOR] |
| Databáze: | Complementary Index |
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