| Autor: |
Kırmızıer, Gizem, Kılınç, Elif Altunel, Yıldırım, Nurdan Oruçoğlu, Türsen, Ümit |
| Předmět: |
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| Zdroj: |
International Journal of Rheumatic Diseases; Mar2024, Vol. 27 Issue 3, p1-5, 5p |
| Abstrakt: |
PASS syndrome is a rare autoinflammatory disease characterized by acne vulgaris, hidradenitis suppurativa, pyoderma gangrenosum, and ankylosing spondylitis. Unlike other autoinflammatory disorders such as PAPA and PASH syndrome, there is no documented gene mutation link. Although there are no established treatment guidelines due to the rarity of these diseases, systemic corticosteroids, biologics, and immunosuppressive drugs are used currently. In our report, we presented a case of PASS syndrome who was unresponsive to adalimumab and in whom we observed improvement in both skin and joint manifestations with intravenous immunoglobulin (IVIG) and anti‐IL‐1 treatment. [ABSTRACT FROM AUTHOR] |
| Databáze: |
Complementary Index |
| Externí odkaz: |
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