| Autor: |
Tekiner, Ayhan, Taşçıoğlu, Tuncer, Yürük, Burak, Gürcan, Zeliha Çulcu, Çiman, Yağmur, Özdemir, Özge |
| Předmět: |
|
| Zdroj: |
Journal of Turkish Spinal Surgery; 2024, Vol. 35 Issue 1, p43-46, 4p |
| Abstrakt: |
Extrarenal Wilms tumor is rare, but its association with spinal dysfraism is even rarer, and to our knowledge, there is no association with meningomyelocele sac in the literature. Our case was a 36-month-old baby with a meningomyelocele sac in the lumbar region. No additional anomaly was detected, and the baby had no leg movements. Magnetic resonance imaging examination revealed a 24x10 mm meningomyelocele sac and an 18x30x27 mm contrast-forming mass in the sac. Mass resection was performed during sac repair. Histological examination revealed a three-phase tumor consisting of a stromal component containing fibrous and fatty tissue, an epithelial component containing primitive glomeruli and tubule structures consisting of papillary structures with fibrovascular nuclei within cystic structures, and a blastemal component containing oval primitive cells between epithelial areas. Immunohistochemically, the blastemal and epithelioid components were stained positively with WT1, the stromal component with vimentin, and the epithelial component with PanCK and EMA. In this form, the case was defined as an extrarenal Wilms tumor associated with a meningocolocele. This case was valuable in terms of showing that Wilms tumor should be included in the differential diagnosis of masses with meningomyelocele and the importance of total resection of these lesions. [ABSTRACT FROM AUTHOR] |
| Databáze: |
Complementary Index |
| Externí odkaz: |
|
