Familial sea -- blue histiocytosis with cutaneous involvement. A case report with ultrastructural findings.

Autor:	Zina, A. M., Bundino, S.
Předmět:	MACROPHAGES RETICULO-endothelial system CONNECTIVE tissue cells MESENCHYME HEMATOPOIETIC system IMMUNOCOMPETENT cells
Zdroj:	British Journal of Dermatology; Mar1983, Vol. 108 Issue 3, p355-361, 7p
Abstrakt:	A 25-year-old man presented with the sea-blue histiocyte syndrome. In addition to hepatosplenomegaly, lung infiltrate and bone marrow involvement, he had cutaneous nodules and plaques over his face, and thickened eyelids. Typical sea-blue histiocytes were found in the skin biopsy. Electron microscopy showed cytoplasmic bodies revealing a peculiar pleomorphic structure. A sister suffered from the same disease. This is the first familial case of sea-blue histiocyte syndrome showing cutaneous involvement. [ABSTRACT FROM AUTHOR]
Databáze:	Complementary Index
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