Hypocomplementemic urticarial vasculitis syndrome presenting with bilateral scleritis.

Autor: Berry, Ella Claire, Wells, Jane, Morey, Adrienne, Anantharajah, Anthea
Zdroj: BMJ Case Reports; Jul2021, Vol. 14 Issue 7, p1-6, 6p
Abstrakt: Hypocomplementemic urticarial vasculitis syndrome (HUVS) is a rare autoimmune disorder characterised by recurrent urticarial lesions and acquired hypocomplementemia with systemic manifestations. The authors present the case of a 70-year-old man who presented to the ophthalmology clinic with bilateral scleritis and ocular hypertension. He was diagnosed with HUVS after a 6-month period of bilateral scleritis, vestibulitis, significant weight loss, mononeuritis multiplex and recurrent urticarial vasculitis with pronounced persistent hypocomplementemia and the presence of anti-C1q antibodies. Disease control was eventually obtained with mycophenolate and prednisolone. [ABSTRACT FROM AUTHOR]
Databáze: Complementary Index