| Autor: |
Хаджийски, П., Янева, П., Байчева, М., Кофинова, Д., Шентова-Енева, Р. |
| Zdroj: |
Pediatria; 7/1/2020, Vol. 60 Issue 3, p35-37, 3p |
| Abstrakt: |
The Syndrome of Budd-Chiari is a rare cause of liver disease including in childhood. Characterized by obstruction of hepatic venous flow which can occur on different level- from the hepatic veins to the atria-empty vein. The syndrome may be primary or secondary, the primary is defined as an obstruction of the lumen of the vessels involved as result of thrombosis, vascular networks or endoflebitis. The secondary syndrome of Budd-Chiari is a result of lesions outside the vessels-tumors, abscesses or cysts which can create a possibility of external compression. In a large percentage of the affected patients is seen a tendency to thrombus formation based on genetic defects in the blood clotting system. The treatment is medicated but if the symptoms are not influenced is possible an intervention procedure. As liver damage progresses, liver transplantation should be considered. [ABSTRACT FROM AUTHOR] |
| Databáze: |
Complementary Index |
| Externí odkaz: |
|
