Congenital hepatic arteriovenous malformation with persistent pulmonary hypertension: an unusual presentation.

Autor: Singh, Yogen, Shore, Hannah
Zdroj: Infant; 2017, Vol. 13 Issue 6, p242-244, 3p, 1 Diagram, 1 Graph
Abstrakt: Congenital hepatic arteriovenous malformations (HAVMs) are rare anomalies, which typically present in infancy with congestive heart failure, anaemia and hepatomegaly. HAVM presenting with persistent pulmonary hypertension of the newborn is extremely rare and associated with high mortality. This case study reports a unique premature infant who developed persistent pulmonary hypertension of the newborn (PPHN) soon after birth. Congenital HAVM was diagnosed by neonatologist-performed echocardiography during evaluation of PPHN and the infant was treated promptly, after which the pulmonary hypertension resolved with excellent outcome. [ABSTRACT FROM AUTHOR]
Databáze: Complementary Index