Primary Hepatic Amyloidosis with Severe Cholestasis: A Case Report.

Autor: Ghalamkari, Marziye, Khatuni, Mahdi, Taher, Mohammad, Khaniki, Mahmood
Zdroj: Iranian Journal of Gastroenterology & Hepatology (GOVARESH); Spring2016, Vol. 21 Issue 1, p76-80, 5p
Abstrakt: Despite the fact that hepatic involvement is frequently seen in systemic primary amyloidosis, major hepatic symptoms as primary manifestation and severe impaired liver function are rare. Herein, we report a 38-year-old woman with primary hepatic amyloidosis, and severe portal hypertension. The patient had ascites and markedly elevated alkaline phosphatase level at presentation. She had a rapid downhill course resulting in death. In case of an unexplained intrahepatic cholestasis or portal hypertension the possibility of amyloidosis should be considered and a Congo red staining should be performed. [ABSTRACT FROM AUTHOR]
Databáze: Complementary Index