| Autor: |
Mankotia, Dipanker Singh, Tandon, Vivek, Sharma, Bhawani Shankar, Rajeshwari, Madhu, Sharma, Mehar Chand |
| Předmět: |
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| Zdroj: |
Journal of Pediatric Neurosciences; Apr-Jun2016, Vol. 11 Issue 2, p121-124, 4p |
| Abstrakt: |
Atypical teratoid/rhabdoid tumor (AT/RT) is a rare central nervous system neoplasm affecting children, and isolated primary spinal involvement is extremely rare. Authors describe a case of spinal AT/RT in a 5‑year‑old male child presenting with rapidly progressing quadriparesis diagnosed and managed surgically and medically. Biopsy revealed large, rhabdoid cells with prominent nucleoli in nest and immunohistochemistry further showed loss of integrase integrator 1 expression considered to be gold standard for diagnosis. AT/RT has extremely poor prognosis with median survival being 6 months. [ABSTRACT FROM AUTHOR] |
| Databáze: |
Complementary Index |
| Externí odkaz: |
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