Sinus dysrhythmia in Kearns-Sayre syndrome.

Autor: Ulicny KS Jr; Department of Surgery, University of North Carolina School of Medicine, Chapel Hill., Detterbeck FC, Hall CD
Jazyk: angličtina
Zdroj: Pacing and clinical electrophysiology : PACE [Pacing Clin Electrophysiol] 1994 May; Vol. 17 (5 Pt 1), pp. 991-4.
DOI: 10.1111/j.1540-8159.1994.tb01445.x
Abstrakt: Kearns-Sayre syndrome is the triad of progressive external ophthalmoplegia, pigmentary retinopathy, and complete AV block. The etiology is unknown, but is thought to be due to a mitochondrial DNA deletion. Reported electrocardiographic abnormalities include first-degree AV block, fascicular blocks, and complete heart block, as well as non-specific S-T segment changes and T wave abnormalities, but has not included sinus node dysfunction. We report a case with episodes of sinus arrest in an asymptomatic patient with Kearns-Sayre syndrome resulting in pauses lasting up to 6 seconds.
Databáze: MEDLINE