| Autor: |
O'Laughlin JC, Bredfeldt JE, Gray JE |
| Jazyk: |
angličtina |
| Zdroj: |
Journal of clinical gastroenterology [J Clin Gastroenterol] 1980 Mar; Vol. 2 (1), pp. 93-8. |
| DOI: |
10.1097/00004836-198003000-00014 |
| Abstrakt: |
The oculopharyngeal syndrome (OPS) is a rare variant of muscular dystrophy characterized by progressive ptosis and dysphagia. Previous esophageal motility studies in OPS have yielded conflicting results because of low-fidelity esophageal recording systems. Although cricopharyngeal myotomy improves symptoms, accurate postoperative manometric findings have not been reported. Using a low-compliance, high-fidelity system and a radially oriented esophageal motility catheter in an OPS patient we found a hypertonic upper esophageal sphincter (UES), a hypotonic proximal esophagus, and elevated pressures in the distal two-thirds with prolonged duration of contraction. Clinical improvement followed myotomy. We also found a similar manometric pattern but a normotensive UES in an asymptomatic sibling. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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