Malignant Peripheral Nerve Sheath Tumor of the Small Bowel: A Case Report and Review of the Literature.

Autor: Ampntin KC; Department of Surgical Oncology, General Anticancer and Oncology Hospital of Athens 'Saint Savvas', Athens, GRC., Tasis N; Department of Surgical Oncology, General Anticancer and Oncology Hospital of Athens 'Saint Savvas', Athens, GRC., Arnaouti M; Department of Pathology, General Anticancer and Oncology Hospital of Athens 'Saint Savvas', Athens, GRC., Chrysi M; Department of Surgical Oncology, General Anticancer and Oncology Hospital of Athens 'Saint Savvas', Athens, GRC., Korkolis DP; Department of Surgical Oncology, General Anticancer and Oncology Hospital of Athens 'Saint Savvas', Athens, GRC., Plastiras A; Department of Surgical Oncology, General Anticancer and Oncology Hospital of Athens 'Saint Savvas', Athens, GRC.
Jazyk: angličtina
Zdroj: Cureus [Cureus] 2024 Dec 05; Vol. 16 (12), pp. e75189. Date of Electronic Publication: 2024 Dec 05 (Print Publication: 2024).
DOI: 10.7759/cureus.75189
Abstrakt: Malignant peripheral nerve sheath tumor (MPNST) is an uncommon type of sarcoma that arises from a peripheral nerve or any tissue with nerve sheath differentiation. It does not have any specific symptoms and shows great variability in clinical and radiological findings. It is usually associated with neurofibromatosis type 1 (NF1). Malignant peripheral nerve sheath tumors mostly originate from soft tissue organs and rarely originate from the small bowel. Less than 20 cases of intestinal MPNSTs are recorded worldwide. Therefore, we present this unique case of a 78-year-old woman, with no history of NF1, who presented with abdominal pain and vomiting and was diagnosed postoperatively with MPNST in the small bowel. Prompted by this case, we reviewed the literature for cases of intestinal MPNSTs.
Competing Interests: Human subjects: Consent for treatment and open access publication was obtained or waived by all participants in this study. Conflicts of interest: In compliance with the ICMJE uniform disclosure form, all authors declare the following: Payment/services info: All authors have declared that no financial support was received from any organization for the submitted work. Financial relationships: All authors have declared that they have no financial relationships at present or within the previous three years with any organizations that might have an interest in the submitted work. Other relationships: All authors have declared that there are no other relationships or activities that could appear to have influenced the submitted work.
(Copyright © 2024, Ampntin et al.)
Databáze: MEDLINE