Long-Term Surgical Success in Treating Vohwinkel Syndrome: A Case Report.

Autor: Bonvillain KW 2nd; Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute-Carolinas Medical Center, Charlotte, North Carolina., Rees AB; Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute-Carolinas Medical Center, Charlotte, North Carolina., Drexelius KD; Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute-Carolinas Medical Center, Charlotte, North Carolina., Serbin R; Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute-Carolinas Medical Center, Charlotte, North Carolina., Aversano MW; OrthoCarolina Hand Center, Charlotte, North Carolina., Gaston RG; Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute-Carolinas Medical Center, Charlotte, North Carolina.; OrthoCarolina Hand Center, Charlotte, North Carolina.
Jazyk: angličtina
Zdroj: JBJS case connector [JBJS Case Connect] 2024 Nov 07; Vol. 14 (4). Date of Electronic Publication: 2024 Nov 07 (Print Publication: 2024).
DOI: e24.00251
Abstrakt: Case: Vohwinkel syndrome is a rare, inherited condition marked by defective keratinization. The disorder may feature digital constriction bands (pseudoainhum) which can lead to autoamputation. Surgical excision is the only treatment of pseudoainhum; however, it is fraught with recurrence. We present a 10-year-old boy with pseudoainhum of the right long and small fingers at the distal interphalangeal joints. He underwent 180-degree band excision and z-plasty.
Conclusion: Since establishing care 8 years ago, he has undergone treatment of 5 constriction bands with only 1 recurrence. We believe this success can at least be partially attributed to the technique described by Upton.
Competing Interests: Disclosure: The Disclosure of Potential Conflicts of Interest forms are provided with the online version of the article (http://links.lww.com/JBJSCC/C478).
(Copyright © 2024 by The Journal of Bone and Joint Surgery, Incorporated.)
Databáze: MEDLINE