Surgical Management of Solitary Extrapulmonary Lymphangioleiomyomatosis in the Mesentery: A Case Report.

Autor:	Menzie J; Department of General Surgery, Monash Health, Melbourne, AUS., Kuan CC; Department of Pathology, Monash Health, Melbourne, AUS., Ackermann T; Department of Upper Gastrointestinal and Hepatobiliary Surgery, Monash Health, Melbourne, AUS., Tay YK; Department of Colorectal Surgery, Monash Health, Melbourne, AUS.
Jazyk:	angličtina
Zdroj:	Cureus [Cureus] 2024 Sep 09; Vol. 16 (9), pp. e69042. Date of Electronic Publication: 2024 Sep 09 (Print Publication: 2024).
DOI:	10.7759/cureus.69042
Abstrakt:	Pulmonary lymphangioleiomyomatosis (LAM) is a rare condition characterised by infiltration of the lungs with abnormal smooth muscles and cystic lesions. A rarer form of the condition is extrapulmonary LAM (E-LAM) where the same cystic lesions are found in various organs throughout the body resulting in a variety of symptoms. Given the rarity of E-LAM and the difficulty in diagnosing it, there is little evidence to guide its management both surgically and medically. We describe a case of a 22-year-old female with a nine-month history of abdominal pain found to have a large mesenteric mass during laparoscopy for suspected ovarian torsion. She underwent a laparotomy to exteriorise the mass and dissect it off the mesentery. The mass was removed without compromise to the bowel or mesentery. The patient recovered well without symptoms and was discharged without complications. Histopathology of the mass revealed it to be E-LAM. This case is the first to our knowledge that demonstrates the successful removal of a solitary E-LAM from the mesentery with minimal adverse outcomes and symptomatic relief. Competing Interests: Human subjects: Consent was obtained or waived by all participants in this study. Conflicts of interest: In compliance with the ICMJE uniform disclosure form, all authors declare the following: Payment/services info: All authors have declared that no financial support was received from any organization for the submitted work. Financial relationships: All authors have declared that they have no financial relationships at present or within the previous three years with any organizations that might have an interest in the submitted work. Other relationships: All authors have declared that there are no other relationships or activities that could appear to have influenced the submitted work. (Copyright © 2024, Menzie et al.)
Databáze:	MEDLINE
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