Beyond Epistaxis: A Rare Case of Ectopic Sinonasal Adamantinomatous Craniopharyngioma.

Autor: Selva Kumaran K; Otolaryngology - Head and Neck Surgery, Hospital Raja Permaisuri Bainun, Ipoh, MYS., Shamsudin NS; Otolaryngology - Head and Neck Surgery, Hospital Tuanku Ja'afar, Seremban, MYS., Dalip Singh HS; Otolaryngology - Head and Neck Surgery, Hospital Raja Permaisuri Bainun, Ipoh, MYS., Devesahayam PR; Otolaryngology - Head and Neck Surgery, Hospital Raja Permaisuri Bainun, Ipoh, MYS.
Jazyk: angličtina
Zdroj: Cureus [Cureus] 2024 Sep 01; Vol. 16 (9), pp. e68357. Date of Electronic Publication: 2024 Sep 01 (Print Publication: 2024).
DOI: 10.7759/cureus.68357
Abstrakt: Adamantinomatous craniopharyngioma (ACP) is one of the two types of craniopharyngioma recognized by the World Health Organization (WHO), the other being papillary craniopharyngioma (PCP). These rare, benign tumours of the pituitary region are classified as Grade 1 central nervous system (CNS) tumours. ACP predominantly affects adolescents aged 5-15 years and adults over 50 years. It is usually located in the sellar and suprasellar regions. We present the case of an 18-year-old Malaysian female with a six-year history of persistent epistaxis and progressive nasal obstruction, an atypical presentation of ACP. This report highlights an entirely ectopic location of ACP in the sinonasal region. The tumour encompassed the left nasal cavity, the left anterior and posterior ethmoid sinuses, and the bilateral frontal sinuses. The unusual presentation of this tumour was detected with the aid of CT and MRI and confirmed by histopathological examination. In this case report, we discuss a rare presentation, an unusual location, and the strategies employed to overcome these challenges.
Competing Interests: Human subjects: Consent was obtained or waived by all participants in this study. Conflicts of interest: In compliance with the ICMJE uniform disclosure form, all authors declare the following: Payment/services info: All authors have declared that no financial support was received from any organization for the submitted work. Financial relationships: All authors have declared that they have no financial relationships at present or within the previous three years with any organizations that might have an interest in the submitted work. Other relationships: All authors have declared that there are no other relationships or activities that could appear to have influenced the submitted work.
(Copyright © 2024, Selva Kumaran et al.)
Databáze: MEDLINE