Suture dehiscence in patients with connective tissue disease: Marfan and Weill-Marchesani syndromes.

Autor: Valentín-Pastrana Aguilar MM; Servicio de Oftalmología, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain. Electronic address: mervpastrana@gmail.com., Platas Moreno I; Hospital Universitario de Getafe, Madrid, Spain., Muñoz Sanz N; Servicio de Oftalmología, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain., Sandoval Cortés B; Servicio de Oftalmología, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain., Herrera Pereiro J; Servicio de Oftalmología, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain., Jiménez-Alfaro Morote I; Servicio de Oftalmología, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain.
Jazyk: angličtina
Zdroj: Archivos de la Sociedad Espanola de Oftalmologia [Arch Soc Esp Oftalmol (Engl Ed)] 2024 Nov; Vol. 99 (11), pp. 512-516. Date of Electronic Publication: 2024 Sep 29.
DOI: 10.1016/j.oftale.2024.09.002
Abstrakt: Marfan and Weill-Marchesani syndromes have a mutation of the fibrillin gene (FBN1), producing alteration of connective tissue, within ophthalmology, it is important to take into consideration this type of diseases in cogenetic alterations in this system will produce modifications at the level of the ocular structures generating problems of various types, Most of the literature refers to ectopia lentis and the complications derived from it, as secondary glaucoma. We present two patients, one with Marfan syndrome and the other with Weill-Marchesani syndrome, who developed lens dislocation, typical of their pathologies, which led them to undergo different surgeries. Both developed suture dehiscence after these surgeries, as a complication derived from their connective tissue involvement. We thus highlight the need for vigilance and extreme caution in the postoperative period of patients affected by this type of syndromes.
(Copyright © 2024 Sociedad Española de Oftalmología. Published by Elsevier España, S.L.U. All rights reserved.)
Databáze: MEDLINE
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