Left Ventricular Non-compaction Cardiomyopathy: A Report of a Rare Case From Saudi Arabia.

Autor:	Irfan Thalib H; General Medicine and Surgery, Batterjee Medical College, Jeddah, SAU., Mehveen S; Genetics, St. Ann's College for Women, Hyderabad, IND., Khan S; General Medicine and Surgery, Batterjee Medical College, Jeddah, SAU., Haidar S; General Medicine and Surgery, Batterjee Medical College, Jeddah, SAU., Jamal A; General Medicine and Surgery, Batterjee Medical College, Jeddah, SAU., Shaikh A; General Medicine and Surgery, Batterjee Medical College, Jeddah, SAU., Alfaqih MA; Internal Medicine, Faculty of Medicine, King Abdulaziz University, Jeddah, SAU., Mansy AA; Cardiology, King Abdullah Medical Complex - Jeddah, Jeddah, SAU.
Jazyk:	angličtina
Zdroj:	Cureus [Cureus] 2024 Jul 19; Vol. 16 (7), pp. e64937. Date of Electronic Publication: 2024 Jul 19 (Print Publication: 2024).
DOI:	10.7759/cureus.64937
Abstrakt:	Left ventricular non-compaction cardiomyopathy (LVNC) is an unusual congenital heart disease that predominantly affects the heart's left ventricle. This disease is characterized by deep intertrabecular recesses and hypertrabeculations of the myocardial wall that link with the ventricle cavity. During embryogenesis, the fetal myocardium has to undergo a compaction process, wherein the trabeculated and spongy myocardial tissue compacts into a dense, solid form. An incomplete compaction process results in persistent non-compacted spongy myocardial tissue and trabeculations prominent in the left ventricle. This disease could be marked alone or be present in coexistence with other congenital heart abnormalities. We present a rare case of a 57-year-old Saudi male who presented to the ER with chest pain and dyspnea. Due to severe chest pain, he was admitted to the coronary care unit. On further investigation, an echocardiogram revealed heavy trabeculations in the dilated left ventricle and a reduced ejection fraction. The case was diagnosed as LVNC and possible heart failure. The patient was discharged after he was kept under guideline-directed medical therapy (GDMT) along with certain medications and will be evaluated after six months of GDMT to decide on implantable cardiac resynchronization therapy. Although LVNC is rare, it can lead to severe heart conditions like arrhythmias, thromboembolism, and heart failure. Competing Interests: Human subjects: Consent was obtained or waived by all participants in this study. Conflicts of interest: In compliance with the ICMJE uniform disclosure form, all authors declare the following: Payment/services info: All authors have declared that no financial support was received from any organization for the submitted work. Financial relationships: All authors have declared that they have no financial relationships at present or within the previous three years with any organizations that might have an interest in the submitted work. Other relationships: All authors have declared that there are no other relationships or activities that could appear to have influenced the submitted work. (Copyright © 2024, Irfan Thalib et al.)
Databáze:	MEDLINE
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