Cerebrofacial Venous Metameric Syndrome Mimicking Vein of Galen Aneurysmal Malformation.

Autor: Demartini Z Jr; Complexo Hospital Pequeno Principe, Curitiba, PR, Brazil; Complexo Hospital de Clínicas, Universidade Federal do Parana, Curitiba, PR, Brazil. Electronic address: demartiniz@gmail.com., Brigid de Zorzi Dalke D; Complexo Hospital de Clínicas, Universidade Federal do Parana, Curitiba, PR, Brazil., Teixeira BCA; Complexo Hospital Pequeno Principe, Curitiba, PR, Brazil; Complexo Hospital de Clínicas, Universidade Federal do Parana, Curitiba, PR, Brazil.
Jazyk: angličtina
Zdroj: World neurosurgery [World Neurosurg] 2024 Oct; Vol. 190, pp. 12-13. Date of Electronic Publication: 2024 Jun 28.
DOI: 10.1016/j.wneu.2024.06.129
Abstrakt: Cerebrofacial venous metameric syndrome (CVMS) is a complex low-flow vascular malformation affecting bone and soft tissues including brain, dura mater, and eye. We show images of CVMS in an 18-month-old boy presenting facial venous malformations, developmental venous anomalies, dural sinus malformations, and dilated great cerebral vein, suggesting a vein of Galen aneurysmal malformation. Although Sturge-Weber syndrome is the most known form of CVMS, its presentations are variable and include several venous malformations. Recognizing the various manifestations of CVMS is necessary for adequate screening, treatment, and follow-up.
(Copyright © 2024 Elsevier Inc. All rights reserved.)
Databáze: MEDLINE
Externí odkaz: