Infant Barlow's Disease in Association with Atrial Septal Defect.

Autor: Silva IA; CardioPedBrasil® - Centro do Coração da Criança at Hospital da Criança e Maternidade São José do Rio Preto, São Paulo, Brazil (FUNFARME/FAMERP)., Matos LAL; CardioPedBrasil® - Centro do Coração da Criança at Hospital da Criança e Maternidade São José do Rio Preto, São Paulo, Brazil (FUNFARME/FAMERP)., Sant'Anna C; CardioPedBrasil® - Centro do Coração da Criança at Hospital da Criança e Maternidade São José do Rio Preto, São Paulo, Brazil (FUNFARME/FAMERP)., Croti UA; CardioPedBrasil® - Centro do Coração da Criança at Hospital da Criança e Maternidade São José do Rio Preto, São Paulo, Brazil (FUNFARME/FAMERP).
Jazyk: angličtina
Zdroj: Brazilian journal of cardiovascular surgery [Braz J Cardiovasc Surg] 2024 May 15; Vol. 39 (4), pp. e20230278. Date of Electronic Publication: 2024 May 15.
DOI: 10.21470/1678-9741-2023-0278
Abstrakt: Clinical Data: Female, seven years old, referred to our service complaining about congestive heart failure symptoms due to mitral valve regurgitation and atrial septal defect. Technical description: Echocardiographic findings compatible with Barlow's disease and atrial septal defect, ostium secundum type.
Operation: She was submitted to mitral valvuloplasty with chordal shortening and prosthetic posterior ring (Gregori-Braile®) along with patch atrioseptoplasty.
Comments: Mitral valve regurgitation is a rare congenital heart disease and Barlow's disease is probably rarer. Mitral valve repair is the treatment of choice.
Databáze: MEDLINE