Diagnostic and therapeutic complexity of Susac syndrome.

Autor: Fierro-Rosales VA; Servicio de Oftalmología, Hospital Clínico Universitario de Salamanca, Salamanca, Spain., de Juan-Marcos L; Servicio de Oftalmología, Hospital Clínico Universitario de Salamanca, Salamanca, Spain; Instituto de Investigación Biomédica de Salamanca (IBSAL), Salamanca, Spain. Electronic address: mloujm@hotmail.com., Bermúdez-Cortés A; Servicio de Oftalmología, Hospital Clínico Universitario de Salamanca, Salamanca, Spain., Lorenzo-Pérez R; Servicio de Oftalmología, Hospital Clínico Universitario de Salamanca, Salamanca, Spain; Instituto de Investigación Biomédica de Salamanca (IBSAL), Salamanca, Spain., Serafim-Reis PM; Servicio de Oftalmología, Hospital Clínico Universitario de Salamanca, Salamanca, Spain.
Jazyk: angličtina
Zdroj: Archivos de la Sociedad Espanola de Oftalmologia [Arch Soc Esp Oftalmol (Engl Ed)] 2024 Aug; Vol. 99 (8), pp. 347-351. Date of Electronic Publication: 2024 May 06.
DOI: 10.1016/j.oftale.2024.05.002
Abstrakt: A 40-year-old man who attended the emergency department with a scotoma in right eye. He mentioned hearing difficulties and headache for months and he had sensory and motor deficits in the previous days. In the ophthalmic examination, the right eye had areas of arterial occlusion. MRI revealed hyperintense lesions. The patient was diagnosed with Susac syndrome. He was treated with systemic steroids, however, it was not enough to control the condition. Rituximab and intravenous immunoglobulins were added, which allowed the improvement of neurological symptoms, but the alteration of the visual field and the hearing defect did not recover. Early diagnosis of this pathology is essential, since delaying treatment can cause irreversible consequences. Sometimes it is difficult given the wide variety of symptoms and the course of the disease. Ocular manifestations may raise suspicion when the general symptoms are nonspecific.
(Copyright © 2024 Sociedad Española de Oftalmología. Published by Elsevier España, S.L.U. All rights reserved.)
Databáze: MEDLINE
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