Arthrogryposis multiplex congenita causing hypercapnic respiratory failure and airway obstruction in an adult patient.

Autor: Bandara H; Northwest Lung Centre Wythenshawe Hospital Manchester UK.; Department of Respiratory Medicine National Hospital for Respiratory Diseases Welisara Sri Lanka., Sathiyamoorthy S; Department of Respiratory Medicine National Hospital for Respiratory Diseases Welisara Sri Lanka., Withana D; Department of Respiratory Medicine National Hospital for Respiratory Diseases Welisara Sri Lanka., Dissanayake T; Department of Respiratory Medicine National Hospital for Respiratory Diseases Welisara Sri Lanka., Athapaththu H; Department of Internal Medicine Base Hospital Nikewaratiya Sri Lanka., Gunasinghe W; Department of Respiratory Medicine National Hospital for Respiratory Diseases Welisara Sri Lanka.
Jazyk: angličtina
Zdroj: Respirology case reports [Respirol Case Rep] 2024 Apr 23; Vol. 12 (4), pp. e01361. Date of Electronic Publication: 2024 Apr 23 (Print Publication: 2024).
DOI: 10.1002/rcr2.1361
Abstrakt: This case highlights arthrogryposis multiplex congenita (AMC) as a rare cause of hypercapnoeic respiratory failure and airway obstruction in adults and emphasizes the usage of leak-port in tracheostomy-NIV (non-invasive-ventilation) specially in resource poor setting when the tracheostomy-NIV mask is unavailable.
Competing Interests: None declared.
(© 2024 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology.)
Databáze: MEDLINE
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