Adult ocular adnexal xanthogranulomatous disease associated with immunoglobulin G4-related disease: an unusual association.

Autor: De Santana AR; Bahiana School of Medicine and Public Health, Salvador. alisson_ios@hotmail.com., Castro de Oliveira Figueirôa MDL; Bahiana School of Medicine and Public Health, Salvador. mariafigueiroa3030@gmail.com., Souza Pedreira AL; Bahiana School of Medicine and Public Health, Salvador. analupedreira@gmail.com., Behrens Pinto GL; Professor Edgard Santos University Hospital Complex, Federal University of Bahia. gustavolbp@gmail.com., Santiago MB; Bahiana School of Medicine and Public Health, Salvador; Professor Edgard Santos University Hospital Complex, Federal University of Bahia; Specialized Rheumatology Services, Bahia. mitter.santiago@serdabahia.com.br.
Jazyk: angličtina
Zdroj: Reumatismo [Reumatismo] 2024 Mar 22; Vol. 76 (1). Date of Electronic Publication: 2024 Mar 22.
DOI: 10.4081/reumatismo.2024.1641
Abstrakt: Adult-onset xanthogranuloma (AOX) and immunoglobulin G4-related disease (IgG4-RD) are uncommon fibrosing conditions that may exhibit localized ocular manifestations and occasionally systemic symptoms. These conditions exhibit overlapping clinical and histological features, suggesting a potential correlation between them, although their exact relationship remains unclear. This paper presents the case of a black male patient exhibiting typical histological indications of both AOX and IgG4-RD. The patient responded positively to corticosteroid treatment.
Databáze: MEDLINE