Rhythmic Jaw Movements in Amyotrophic Lateral Sclerosis: Is It Clonus or Tremor?

Autor: Kumar R; Department of Neurology, Norman Fixel Institute for Neurological Diseases, University of Florida, Gainesville, Florida, United States of America., Blackband J; Department of Neurology, Norman Fixel Institute for Neurological Diseases, University of Florida, Gainesville, Florida, United States of America., Wagle Shukla A; Department of Neurology, Norman Fixel Institute for Neurological Diseases, University of Florida, Gainesville, Florida, United States of America.
Jazyk: angličtina
Zdroj: Tremor and other hyperkinetic movements (New York, N.Y.) [Tremor Other Hyperkinet Mov (N Y)] 2024 Feb 29; Vol. 14, pp. 8. Date of Electronic Publication: 2024 Feb 29 (Print Publication: 2024).
DOI: 10.5334/tohm.845
Abstrakt: Background: Jaw clonus refers to involuntary, rhythmic jaw contractions induced by a hyperactive trigeminal nerve stretch reflex; however, the movements, when triggered without a stretch, can be confused with a tremor.
Phenomenology Shown: This video demonstrates a patient with amyotrophic lateral sclerosis presenting with rapid rhythmic jaw movements seen at rest, alongside a power spectrum analysis revealing a narrow high-frequency peak of 10 Hz.
Educational Value: Rhythmic jaw movements are seen in many disorders such as Parkinson's disease, essential tremor, tardive syndromes, and cranial myorhythmias; however, a high-frequency movement, regardless of clonus or tremor, can indicate amyotrophic lateral sclerosis when accompanied by typical upper and lower motor neuron signs.
Highlights: The presented video abstract shows a patient with amyotrophic lateral sclerosis with rhythmic jaw movements seen at rest. A power spectrum analysis of the rhythmic movements revealed a 10 Hz peak, a frequency higher than those seen in patients with Parkinson's disease, essential tremor, myorhythmia, and tardive syndromes.
Competing Interests: The authors have no competing interests to declare.
(Copyright: © 2024 The Author(s).)
Databáze: MEDLINE