Severe Multilevel Tracheal Stenosis with Significant Twisting in a Patient with Spondylometaphyseal Dysplasia: A Case Report.

Autor:	Stefko JM; From the Department of Anesthesiology, Sidney Kimmel Medical College at Thomas Jefferson University Hospital, Philadelphia, Pennsylvania., Oommen A; Department of Anesthesiology, Nemours Children's Health, Wilmington, Delaware., Jones J; Department of Anesthesiology, Nemours Children's Health, Wilmington, Delaware., Arai L; Department of Anesthesiology, Nemours Children's Health, Wilmington, Delaware., Dicindio S; Department of Anesthesiology, Nemours Children's Health, Wilmington, Delaware., Theroux M; Department of Anesthesiology, Nemours Children's Health, Wilmington, Delaware.
Jazyk:	angličtina
Zdroj:	A&A practice [A A Pract] 2024 Feb 27; Vol. 18 (3), pp. e01759. Date of Electronic Publication: 2024 Feb 27 (Print Publication: 2024).
DOI:	10.1213/XAA.0000000000001759
Abstrakt:	Spondylometaphyseal dysplasia (SMD) is a rare genetic disorder affecting skeletal growth and development presenting anesthesiologists with many perioperative challenges. We present a case of a patient found to have multilevel tracheal stenosis due to twisting and folding of his trachea. This was discovered on imaging during a research review of SMD cases at our institution. Structural and functional abnormalities of the trachea have not been reported in SMD. This is the first description of a patient with SMD with severe multilevel tracheal disease requiring tracheal reconstructive surgery. Competing Interests: The authors declare no conflicts of interest. (Copyright © 2024 International Anesthesia Research Society.)
Databáze:	MEDLINE
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