Airway management of a child with mucopolysaccharidosis undergoing cervical spine surgery: A case report.
| Autor: | Elbashary AS; Department of Anesthesia, King Saud University Medical City, Riyadh, Kingdom of Saudi Arabia., Kanchi NU; Department of Anesthesia, King Saud University Medical City, Riyadh, Kingdom of Saudi Arabia., Delvi MB; Department of Anesthesia, King Saud University Medical City, Riyadh, Kingdom of Saudi Arabia., Alhatlan AI; Department of Anesthesia, King Saud University Medical City, Riyadh, Kingdom of Saudi Arabia. |
|---|---|
| Jazyk: | angličtina |
| Zdroj: | Saudi journal of anaesthesia [Saudi J Anaesth] 2024 Jan-Mar; Vol. 18 (1), pp. 129-130. Date of Electronic Publication: 2024 Jan 02. |
| DOI: | 10.4103/sja.sja_515_23 |
| Abstrakt: | "Mucopolysaccharidosis" (MPS) is a rare, autosomal recessive lysosomal storage disease characterized by deficiencies in 11 different lysosomal enzymes involved in the metabolism of glycosaminoglycans (GAGs) leading to its accumulation, the condition which results in anatomic abnormalities and multi-organ dysfunction that increases the risk of anesthesia complications. The patterns of accumulation form the basis of MPS classification into seven types of progressive diseases. Most of the MPS types have facial and oral characteristics that increase the risk of airway management. We are reporting a case of MPS with a challenging airway, an 11-years-old boy diagnosed with MPS type VI with a prominent facial character planned for cervical spine fixation versus decompression, successfully managed with fiberoptic bronchoscopy (FOB) guided by video laryngoscopy (VL). Competing Interests: There are no conflicts of interest. (Copyright: © 2023 Saudi Journal of Anesthesia.) |
| Databáze: | MEDLINE |
| Externí odkaz: |
|