Hughes-Stovin Syndrome: A Case Report on a Rare, Life-Threatening Vasculitis.

Autor:	Khursheed T; Department of Rheumatology, Pakistan Institute of Medical Sciences, Islamabad, Pakistan., Masood A; Department of Rheumatology, Pakistan Institute of Medical Sciences, Islamabad, Pakistan., Khan MS; Department of Rheumatology, Pakistan Institute of Medical Sciences, Islamabad, Pakistan., Sharif M; Department of Rheumatology, Pakistan Institute of Medical Sciences, Islamabad, Pakistan., Shah S; Department of Rheumatology, Pakistan Institute of Medical Sciences, Islamabad, Pakistan., Miraj MA; Department of Rheumatology, Pakistan Institute of Medical Sciences, Islamabad, Pakistan.
Jazyk:	angličtina
Zdroj:	Mediterranean journal of rheumatology [Mediterr J Rheumatol] 2023 Aug 29; Vol. 34 (4), pp. 565-569. Date of Electronic Publication: 2023 Aug 29 (Print Publication: 2023).
DOI:	10.31138/mjr.290823.hsr
Abstrakt:	Hughes-Stovin Syndrome (HSS) is a rare vasculitic disorder characterised by widespread pulmonary artery aneurysms. It shares some features with Behçet disease. Currently, the diagnosis is based on clinical suspicion. Our case describes a young male who presented with haemoptysis and previous history of pulmonary embolism. Workup was essentially unremarkable, but imaging revealed multiple pulmonary artery aneurysms. Timely initiation of glucocorticoids and immunosuppression with cyclophosphamide led to improvement. High-dose glucocorticoids and immunosuppressants are the mainstays of treatment. Untreated cases can result in fatal outcomes. Competing Interests: The Author Team has no conflict of interest to declare. (© 2023 The Mediterranean Journal of Rheumatology (MJR).)
Databáze:	MEDLINE
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