Aorta Without Coronary Arteries: Anatomic Variants of a Rare Malformation.

Autor: Karila-Cohen J; Medical and Surgical Unit of Congenital and Paediatric Cardiology, Reference Centre for Complex Congenital Heart Defects - M3C, University Hospital Necker-Enfants Malades, Paris, France. julie.karila-cohen@aphp.fr., Laux D; Medical and Surgical Unit of Congenital and Paediatric Cardiology, Reference Centre for Complex Congenital Heart Defects - M3C, University Hospital Necker-Enfants Malades, Paris, France., Houyel L; Medical and Surgical Unit of Congenital and Paediatric Cardiology, Reference Centre for Complex Congenital Heart Defects - M3C, University Hospital Necker-Enfants Malades, Paris, France.; University Paris Cité, Paris, France., Bonnet D; Medical and Surgical Unit of Congenital and Paediatric Cardiology, Reference Centre for Complex Congenital Heart Defects - M3C, University Hospital Necker-Enfants Malades, Paris, France.; University Paris Cité, Paris, France.
Jazyk: angličtina
Zdroj: Pediatric cardiology [Pediatr Cardiol] 2024 Jan; Vol. 45 (1), pp. 200-207. Date of Electronic Publication: 2023 Nov 07.
DOI: 10.1007/s00246-023-03330-7
Abstrakt: Absence of connection of both coronary arteries to the aorta is an extremely rare congenital malformation. Most cases reported are anatomic variants of anomalous left coronary artery to pulmonary artery, found in isolation or in association with other congenital heart defects. We describe here four cases of patients born without any coronary artery connected to the aorta, including two with an almost complete absence of epicardial coronary arteries, one with single coronary artery to the right pulmonary artery, and one with left ventricular connection of a single coronary artery. Those exceptional coronary malformations have a poor prognosis and are often diagnosed at autopsy. Total absence of epicardial coronary arteries, present in two of our patients and described only once in the literature, leads us to reconsider current knowledge of human coronary artery development.
(© 2023. The Author(s), under exclusive licence to Springer Science+Business Media, LLC, part of Springer Nature.)
Databáze: MEDLINE
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