Ewing sarcoma of the temporal bone with aneurysmal bone cyst-like changes: A rare case report with an unusual radiological presentation.

Autor: Lloret I; Department of Radiology, The Norwegian Radium Hospital, Oslo University Hospital, Norway., Hompland I; Department of Oncology, The Norwegian Radium Hospital, Oslo University Hospital, Norway., Lobmaier IV; Department of Pathology, The Norwegian Radium Hospital, Oslo University Hospital, Norway., Sundseth J; Department of Neurosurgery, Rikshospitalet, Oslo University Hospital, Norway., Server A; Section of Neuroradiology, Department of Radiology, Rikshospitalet, Oslo University Hospital, Norway.
Jazyk: angličtina
Zdroj: The neuroradiology journal [Neuroradiol J] 2024 Oct; Vol. 37 (5), pp. 640-644. Date of Electronic Publication: 2023 Nov 03.
DOI: 10.1177/19714009231212358
Abstrakt: Ewing sarcoma (ES) is a malignant small round cell tumor, accounting for 10-15% of all primary bone tumors and approximately 3% of all pediatric cancers. Primary ES of the cranial bone is unusual with reported incidence from 1% to 6% of all ES cases. This report shows a rare case of primary ES of the squamous temporal bone in a 12-year-old boy with a history of swelling of the right temporal region and symptoms of increased intracranial pressure. We illustrate the extremely unusual radiological presentation of this primary ES of temporal bone associated with large aneurysmal bone cyst-like (ABC-like) changes. The boy was successfully treated according to Euro Ewing 2012 protocol. He is alive with no evidence of recurrence and metastasis after 16 months of completed treatment.
Competing Interests: Declaration of conflicting interestsThe authors declare no potential conflict of interest with respect to the research, authorship, and/or publication of this article.
Databáze: MEDLINE