Severe Aortic Valvular Incompetence From IgG4-Related Disease: An Unusual Entity.

Autor: Soh BWT; Department of Cardiology, University Hospital Limerick, Limerick, Ireland., Prendergast SC; Department of Histopathology, Cork University Hospital, Cork, Ireland., Burke L; Department of Histopathology, Cork University Hospital, Cork, Ireland., O'Connor CT; Department of Cardiology, University Hospital Limerick, Limerick, Ireland., Ullah I; Department of Cardiology, University Hospital Limerick, Limerick, Ireland., O'Brien JM; Department of Radiology, University Hospital Limerick, Limerick, Ireland., Hinchion JA; Department of Cardiothoracic Surgery, Cork University Hospital, Cork, Ireland., Arnous S; Department of Cardiology, University Hospital Limerick, Limerick, Ireland., Kiernan TJ; Department of Cardiology, University Hospital Limerick, Limerick, Ireland.; School of Medicine, University of Limerick, Limerick, Ireland.
Jazyk: angličtina
Zdroj: JACC. Case reports [JACC Case Rep] 2023 Sep 15; Vol. 24, pp. 102027. Date of Electronic Publication: 2023 Sep 15 (Print Publication: 2023).
DOI: 10.1016/j.jaccas.2023.102027
Abstrakt: IgG4-related disease (IgG4-RD) is a new clinical entity characterized by lymphoplasmacytic lesions rich in IgG4-positive plasma cells. Myocardial involvement is extremely rare and not a typical cardiovascular manifestation of IgG4-RD. We report a rare case of IgG4-RD-associated myocardial mass causing severe aortic incompetence, successfully treated with surgery and corticosteroids. ( Level of Difficulty: Intermediate. ).
Competing Interests: The authors have reported that they have no relationships relevant to the contents of this paper to disclose.
(© 2023 The Authors.)
Databáze: MEDLINE