Susac syndrome: a case report with initial presentation of incomplete bitemporal hemianopia.

Autor: Gunaratnam C; Department of Neurology, Townsville University Hospital, Townsville 4810, Australia.; School of Medicine, University of Queensland, Brisbane 4006, Australia.; School of Medicine, University of Sydney, New South Wales 2056, Australia., King T; Faculty of Medicine, James Cook University, Townsville 4810, Australia., Moloney TP; School of Medicine, University of Queensland, Brisbane 4006, Australia.; Department of Ophthalmology, Royal Brisbane and Womens Hospital, Brisbane 4006, Australia., Boggild M; Department of Neurology, Townsville University Hospital, Townsville 4810, Australia., Goodwin T; Faculty of Medicine, James Cook University, Townsville 4810, Australia.; NQ Eye Foundation, Townsville 4812, Australia.
Jazyk: angličtina
Zdroj: Journal of surgical case reports [J Surg Case Rep] 2023 Oct 18; Vol. 2023 (10), pp. rjad541. Date of Electronic Publication: 2023 Oct 18 (Print Publication: 2023).
DOI: 10.1093/jscr/rjad541
Abstrakt: Susac syndrome (SS) is a rare microangiopathy affecting the precapillary arterioles of the brain, inner ear, and retina. We present a novel case of SS, presenting as acute incomplete bitemporal field loss in addition to temporally spaced neurological and vestibulocochlear symptoms. A 39-year-old female was referred to the ophthalmology clinic with acute incomplete bitemporal hemianopia and worsening hemicrania. History revealed progressive hearing loss, subjective short-term memory impairment, and vertigo temporally spaced over the preceding 12 months. Magnetic resonance brain revealed multiple small colosal lesions and liner 'spoke' lesions. Fundus fluorescein angiography revealed multiple branch retinal artery occlusions in the right eye. Audiometry confirmed bilateral sensorineural hearing loss. Treatment included intravenous corticosteroids and rituximab. This case highlights the importance of early consideration and evaluation of SS in individuals presenting with atypical ocular disturbances, where no clear cause can be elicited, in order to limit the sequelae of disease.
Competing Interests: None declared.
(Published by Oxford University Press and JSCR Publishing Ltd. © The Author(s) 2023.)
Databáze: MEDLINE
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