Ulnar dimelia - a review of 24 cases.

Autor: Winge MI; Division of Orthopaedic Surgery, Oslo University Hospital, Oslo, Norway., Guéro S; Institut de la main, Clinique Bizet, Paris, France., Zavarukhin V; Saint Petersburg State University Hospital, Vasilievsky island, Saint-Petersburg, Russia., Paavilainen P; Tampere University Hospital, Central Hospital, Tampere, Finland., Baldrighi C; Al Jalila Children's Specialty Hospital, Dubai, UAE., Kjørup A; Rigshospitalet, Copenhagen, Denmark., Hülsemann W; Children`s Hospital Wilhelmstift, Handsurgery Department, Hamburg, Germany.
Jazyk: angličtina
Zdroj: The Journal of hand surgery, European volume [J Hand Surg Eur Vol] 2023 Dec; Vol. 48 (11), pp. 1126-1135. Date of Electronic Publication: 2023 Sep 08.
DOI: 10.1177/17531934231196418
Abstrakt: Ulnar dimelia is a very rare unilateral congenital upper limb anomaly (CULA) affecting the whole extremity. Treatment remains difficult because of the complexity and multi-level involvement. Twenty-four cases with duplicated ulna, absent radius and polydactyly from seven European centres were reviewed according to a structured list of parameters. At first consultation, median age 8 months (1-178), the shoulder movement was good in 17 patients or poor in six, and the median passive elbow range of motion was 20° (0°-90°). The resting wrist position was flexed in 22/24 patients. Following stretching and splinting, elbow surgery included resection of the lateral proximal ulna in 11 patients and muscle transfers in six to improve passive movement and increase active elbow motion, respectively. Tendon transfers were performed in eight wrists and a pollicization or pseudo-pollicization in 23 patients. Overall, patients demonstrate acceptable function postoperatively. Guidelines for treatment of this severe CULA are presented. Level of evidence: IV.
Competing Interests: Declaration of conflicting interestsThe authors declare no potential conflicts of interest with respect to the research, authorship, and/or publication of this article.
Databáze: MEDLINE