Anesthetic Considerations for an Adult With Bannayan-Riley-Ruvalcaba Syndrome: A Case Report.

Autor: Pivalizza CM; From the Department of Anesthesiology, McGovern Medical School, UTHouston, Houston, Texas., Jefferies HB, Pivalizza EG
Jazyk: angličtina
Zdroj: A&A practice [A A Pract] 2023 Jul 05; Vol. 17 (7), pp. e01690. Date of Electronic Publication: 2023 Jul 05 (Print Publication: 2023).
DOI: 10.1213/XAA.0000000000001690
Abstrakt: Anesthetic considerations for adults with Bannayan-Riley-Ruvalcaba syndrome, part of the PTEN (phosphatase and tensin homolog) hamartoma tumor syndrome, are not well described. As patients may require surgical intervention for associated musculoskeletal, intestinal, oncologic, or soft tissue masses, knowledge of implications of anesthesia is necessary. Airway management may be challenging given macrocephaly and accumulation of lymphangiomatous tissue in the oro/hypopharynx. This report describes a patient with typical features, nonreassuring external airway anatomy, and developmental delay, which precluded an awake airway management technique. The airway was secured with the use of high-flow nasal oxygen and videolaryngoscopy.
Competing Interests: Conflicts of Interest: See Disclosures at the end of the article.
(Copyright © 2023 International Anesthesia Research Society.)
Databáze: MEDLINE