A rare case report of pancreatic low-grade fibromyxoid sarcoma (LGFMS).

Autor: Weiler EJ; Sparrow Hospital, 1200 E, Michigan Ave, #255, Lansing, MI, 48912, USA. ericjweiler@gmail.com., Murickan T; University of Nebraska Medical Center, 983285 Nebraska Medical Center, Omaha, NE, 68198, USA., Drayer CN; UnityPoint Clinic General Surgery, 2730 Pierce St. Suite 402, Sioux City, IA, 51104, USA., Samat SH; Sparrow Hospital, 1200 E, Michigan Ave, #255, Lansing, MI, 48912, USA., Kia MA; McLaren Hospital, 3500 Calkins Rd, Flint, MI, 48532, USA.
Jazyk: angličtina
Zdroj: Surgical case reports [Surg Case Rep] 2023 Jul 03; Vol. 9 (1), pp. 123. Date of Electronic Publication: 2023 Jul 03.
DOI: 10.1186/s40792-023-01662-3
Abstrakt: Background: Low-grade fibromyxoid sarcoma (LGFMS) is an uncommon neoplasm generally affecting muscle tissue. It presents rarely in abdominal viscera and even more rarely occurs in the pancreas. All types of pancreatic sarcomas are uncommon, and LGFMS is a rarer still. We present the case of an LGFMS in the pancreas. Because of its rarity, there are no guidelines for appropriate treatment or summations of the natural course of this illness.
Case Presentation: We present the case of a 49-year-old female who presented with epigastric pain. She had a prior history of three episodes of acute pancreatitis many years earlier. A CT revealed a pancreatic body mass, which was biopsied. Pathology returned LGFMS. The patient underwent a distal pancreatectomy and splenectomy. She did well after the case and did not require further intervention.
Conclusion: Though it is exceedingly rare, cases of pancreatic LGFMS should be reported in order to guide clinical decisions. LGFMS has been shown to have high malignant potential in other tissues, and there is no reason to think pancreatic masses will be different. By building a body of evidence about these rare tumors, patient care will benefit.
(© 2023. The Author(s).)
Databáze: MEDLINE
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