An Unusual Case of Macrophage Activation Syndrome (MAS)- Hemophagocytic Lymphohistiocytosis (HLH) Triggered by Necrotizing Autoimmune Myopathy.
| Autor: | Brown TS; Internal Medicine, Louisiana State University Health Sciences Center, Shreveport, USA., Vo G; Critical Care Medicine, Louisiana State University Health Sciences Center, Shreveport, USA., Charoenpong P; Pulmonology and Critical Care, Louisiana State University Health Sciences Center, Shreveport, USA. |
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| Jazyk: | angličtina |
| Zdroj: | Cureus [Cureus] 2023 May 03; Vol. 15 (5), pp. e38501. Date of Electronic Publication: 2023 May 03 (Print Publication: 2023). |
| DOI: | 10.7759/cureus.38501 |
| Abstrakt: | Macrophage activation syndrome (MAS)- hemophagocytic lymphohistiocytosis (HLH) secondary to inflammatory myopathies such as dermatomyositis (DM), polymyositis (PM), and necrotizing autoimmune myopathy is exceedingly rare in the medical literature. We present the complicated diagnosis and treatment of a 41-year-old female who presented with proximal muscle weakness and shock. Following an extensive critical care workup, she was diagnosed with MAS-HLH, triggered by a newly diagnosed necrotizing autoimmune myopathy. In this case report and literature review, we would like to highlight the importance of recognizing the clinical signs of MAS-HLH in rheumatological disorders and the necessity for rapid treatment. Competing Interests: The authors have declared that no competing interests exist. (Copyright © 2023, Brown et al.) |
| Databáze: | MEDLINE |
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