Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report.

Autor: Lo A; School of Medicine, University of California, Irvine, Irvine, CA, USA., LaRocca MC; School of Medicine, University of California, Irvine, Irvine, CA, USA., Whalen D; Department of Child Neurology, Children's Hospital Orange County, Orange, CA, USA., Gonzalez-Castillo Z; Department of Child Neurology, Children's Hospital Orange County, Orange, CA, USA.
Jazyk: angličtina
Zdroj: Child neurology open [Child Neurol Open] 2023 Apr 26; Vol. 10, pp. 2329048X231169510. Date of Electronic Publication: 2023 Apr 26 (Print Publication: 2023).
DOI: 10.1177/2329048X231169510
Abstrakt: Chiari malformation is a clinico-radiological entity defined by herniation of rhombencephalic structures through the foramen magnum. The most common type, Chiari I, involves herniation of the cerebellar tonsils specifically. We present the case of a 2-year-old with three weeks of progressive bilateral leg weakness, absent reflexes, and the inability to walk. The patient was found to have Chiari I with hydrocephalus and syringomyelia. This is the youngest patient reported in the literature presenting with a clinical picture of spinal shock. Early recognition of this entity allows for proper treatment and improved outcomes.
Competing Interests: The author(s) declared no potential conflicts of interest with respect to the research, authorship, and/or publication of this article.
(© The Author(s) 2023.)
Databáze: MEDLINE