EPILEPTIC SEIZURES REVEALING STURGE WEBER'S DISEASE IN A TROPICAL ENVIRONMENT: STUDY OF EIGHT CASES.

Autor:	Touré ML; 1Department of Neurology, University of Conakry, Guinea., Othon GC; 1Department of Neurology, University of Conakry, Guinea., Diallo SM; 1Department of Neurology, University of Conakry, Guinea., Baldé TH; 1Department of Neurology, University of Conakry, Guinea., Barry SD; 1Department of Neurology, University of Conakry, Guinea., Konaté MM; 4Department of Neurology, National Hospital, Niamey, Niger., Sakadi F; 5Neurology Department, Reference Hospital, N'Djamena, Chad., Kassa FD; 1Department of Neurology, University of Conakry, Guinea., Kourouma A; 6Department of Ondontostomatology, University of Conakry, Guinea., Kadji JM; 1Department of Neurology, University of Conakry, Guinea., Diakité M; 2Department of Hematology, University of Conakry, Guinea., Sakho A; 3Department of Radiology, University of Conakry, Guinea., Diallo MT; 1Department of Neurology, University of Conakry, Guinea., Condé S; 1Department of Neurology, University of Conakry, Guinea., Millimono V; 1Department of Neurology, University of Conakry, Guinea., Camara D; 1Department of Neurology, University of Conakry, Guinea., Madandi H; 1Department of Neurology, University of Conakry, Guinea., Diallo TM; 1Department of Neurology, University of Conakry, Guinea., Lamah E; 1Department of Neurology, University of Conakry, Guinea., Cisse FA; 1Department of Neurology, University of Conakry, Guinea., Cisse A; 1Department of Neurology, University of Conakry, Guinea.
Jazyk:	angličtina
Zdroj:	Georgian medical news [Georgian Med News] 2023 Jan (334), pp. 116-124.
Abstrakt:	In sub-Saharan Africa (SSA), the etiological factors of epilepsy are multiple and phacomatoses, in particular Sturge weber's disease, are rarely reported due to under-medicalization and insufficient multidisciplinary care. We carried out a retrospective study of 216 patients hospitalized for recurrent epileptic seizures between 2015 and 2022 in the neurology and pediatrics department of the University Hospital Center of Conakry, among whom eight (8) patients were identified for Sturge Weber's disease in order to reassess this pathology from a clinical and paraclinical point of view in a tropical environment. Sturge Weber's disease was retained in eight (8) on the presence of symptomatic partial epileptic seizures (age 6 months to 14 years) with frequency of status epilepticus, homonymous lateral hemiparesis linked to occipital involvement, piriform calcifications on imaging and ocular disorders. The delay in consultation and medical care revealed severe mental deterioration in our patients. This study shows a stereotyped clinical picture in a context of aggravation of signs related to a delay in multidisciplinary management. These results are important for the diagnostic, therapeutic and prognostic discussion.
Databáze:	MEDLINE
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