Hepatic Perivascular Epithelioid Cell Tumor Mimicking Hepatocellular Carcinoma.

Autor: Harwal R; Institute of Surgical Gastroenterology, Madras Medical College and Rajiv Gandhi Government General Hospital, Chennai, India., Joseph Rosemary LJ; Institute of Surgical Gastroenterology, Madras Medical College and Rajiv Gandhi Government General Hospital, Chennai, India., Raju P; Institute of Surgical Gastroenterology, Madras Medical College and Rajiv Gandhi Government General Hospital, Chennai, India., Chidambaranathan S; Institute of Surgical Gastroenterology, Madras Medical College and Rajiv Gandhi Government General Hospital, Chennai, India., Bharathi Vidya Jayanthi J; Institute of Surgical Gastroenterology, Madras Medical College and Rajiv Gandhi Government General Hospital, Chennai, India., Obla Lakshmanamoorthy NB; Institute of Surgical Gastroenterology, Madras Medical College and Rajiv Gandhi Government General Hospital, Chennai, India.
Jazyk: angličtina
Zdroj: ACG case reports journal [ACG Case Rep J] 2023 Jan 20; Vol. 10 (1), pp. e00962. Date of Electronic Publication: 2023 Jan 20 (Print Publication: 2023).
DOI: 10.14309/crj.0000000000000962
Abstrakt: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms, and liver PEComas are extremely rare. They are usually discovered incidentally, and diagnostic pitfalls are frequent owing to similar imaging characteristics to other liver neoplasms. We present a patient whose evaluation was consistent with a right-sided hepatocellular carcinoma for which right hepatectomy was performed. Based on the final histopathological examination and immunohistochemistry, a diagnosis of PEComa was made. Immunohistochemistry plays a crucial role in arriving at the diagnosis, and resection represents the standard of care. A long-term follow-up is recommended because the natural history of PEComas is unpredictable.
(© 2023 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of The American College of Gastroenterology.)
Databáze: MEDLINE