A Rare Case of Left Ventricular Malignant Peripheral Nerve Sheath Tumour-Case Report and Review of the Literature.

Autor: Moldovan H; Faculty of Medicine, Carol Davila University of Medicine and Pharmacy, 050474 Bucharest, Romania.; Department of Cardiovascular Surgery, Emergency Clinical Hospital Bucharest, 014461 Bucharest, Romania.; Academy of Romanian Scientists, 54, Spl. Independentei, 050711 Bucharest, Romania., Ciomaga I; Department of Cardiovascular Surgery, Sanador Clinical Hospital, 010991 Bucharest, Romania., Nechifor E; Department of Cardiovascular Surgery, Sanador Clinical Hospital, 010991 Bucharest, Romania., Tigănașu R; Department of Cardiovascular Surgery, Emergency Clinical Hospital Bucharest, 014461 Bucharest, Romania., Badea A; Department of Cardiovascular Surgery, Emergency Clinical Hospital Bucharest, 014461 Bucharest, Romania., Dobra I; Department of Cardiovascular Surgery, Emergency Clinical Hospital Bucharest, 014461 Bucharest, Romania., Nica C; Department of Cardiovascular Surgery, Emergency Clinical Hospital Bucharest, 014461 Bucharest, Romania., Scarlat C; Department of Cardiovascular Surgery, Sanador Clinical Hospital, 010991 Bucharest, Romania., Gheorghiță D; Faculty of Materials Science and Engineering, Politehnica University of Bucharest, 060042 Bucharest, Romania., Antoniac I; Academy of Romanian Scientists, 54, Spl. Independentei, 050711 Bucharest, Romania.; Faculty of Materials Science and Engineering, Politehnica University of Bucharest, 060042 Bucharest, Romania., Zaharia O; Faculty of Medicine, Carol Davila University of Medicine and Pharmacy, 050474 Bucharest, Romania.; Department of Internal Medicine, Prof. Dr. Theodor Burghele Clinical Hospital, 050659 Bucharest, Romania.
Jazyk: angličtina
Zdroj: Medicina (Kaunas, Lithuania) [Medicina (Kaunas)] 2022 Oct 06; Vol. 58 (10). Date of Electronic Publication: 2022 Oct 06.
DOI: 10.3390/medicina58101404
Abstrakt: Malignant peripheral nerve sheath tumour (MPNST) is an aggressive and uncommon cancer developing in the peripheral nerve sheath. Primary cardiac MPNST is an extremely rare finding, with no specific imaging and clinical characteristics. Only a handful of cases have been reported in the literature; thus, little is still known about them. Cardiac computed tomography (CT) and cardiac magnetic resonance imaging (CMRI) are important means of assessing cardiac morphology and function. The preferred course of treatment for this pathology is by full surgical resection of the tumour, with negative (clear) margins, followed by adjuvant radiotherapy and chemotherapy. We present the case of a 42-year-old woman with no significant cardiovascular symptoms who was incidentally diagnosed during routine transthoracic echocardiography (TTE) with a cardiac mass located in the left ventricle.
Databáze: MEDLINE
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