[Treatment of thrombotic thrombocytopenic purpura].

Autor: Galstyan GM; National Research Center for Hematology., Maschan AA; Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology., Klebanova EE; National Research Center for Hematology., Kalinina II; Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology.
Jazyk: ruština
Zdroj: Terapevticheskii arkhiv [Ter Arkh] 2021 Jul 23; Vol. 93 (7), pp. 826-829. Date of Electronic Publication: 2021 Jul 23.
DOI: 10.26442/00403660.2021.07.200914
Abstrakt: The review discusses approaches to treatment of congenital thrombotic thrombocytopenic purpura (TTP) or Upshaw-Schulman syndrome. In congenital TTP, plasma transfusions are sufficient. Such treatment options as plasma exchange, administration of clotting factor VIII concentrate, recombinant ADAMTS13, are also used. Separately discussed issues of management of patients with TTP during pregnancy, and pediatric patients with TTP.
Databáze: MEDLINE